Indian Journal of Ophthalmology - Case Reports

OPHTHALMIC IMAGE
Year
: 2021  |  Volume : 1  |  Issue : 3  |  Page : 452-

Quadrantic lamellar lens opacity - Rule out Stickler!


Vanshaj Rai1, Aditi Parab1, Priya Sivakumar2,  
1 Department of Ophthalmology, Aravind Eye Hospital, Puducherry, India
2 Department of Neuro Ophthalmology and Low Vision Services, Aravind Eye Care, Puducherry, India

Correspondence Address:
Dr. Priya Sivakumar
Department of Neuro Ophthalmology and Low Vision Services, Aravind Eye Care, Puducherry - 605 007
India




How to cite this article:
Rai V, Parab A, Sivakumar P. Quadrantic lamellar lens opacity - Rule out Stickler!.Indian J Ophthalmol Case Rep 2021;1:452-452


How to cite this URL:
Rai V, Parab A, Sivakumar P. Quadrantic lamellar lens opacity - Rule out Stickler!. Indian J Ophthalmol Case Rep [serial online] 2021 [cited 2021 Oct 19 ];1:452-452
Available from: https://www.ijoreports.in/text.asp?2021/1/3/452/319979


Full Text



A 34-year-old man presented with complaints of defective vision in both eyes with no known systemic illness and no history of trauma. His BCVA in right eye was 6/12 and in left eye was 6/9. Anterior segment examination revealed bilateral temporal lamellar cortical lenticular opacity [Figure 1]a and [Figure 1]b, characteristic sign of Stickler syndrome.[1] Other features of stickler syndrome are multiple pigmented radial lattices on retina,[2] congenital myopia,[1] glaucoma due to angle anomalies,[1] typical facial features consists of mid-facial hypoplasia, depressed nasal bridge, micrognathia and anteverted nares,[3] musculoskeletal features include joint spondyloperipheral dysplasia, hypermotility and early-onset osteoarthritis,[4] hearing loss.[1] Bilateral zonal cataracts are usually idiopathic but are also associated with hereditary disorders and maternal vitamin D deficiency.[5]{Figure 1}

Declaration of patient consent

The authors certify that they have obtained all appropriate patient consent forms. In the form the patient(s) has/have given his/her/their consent for his/her/their images and other clinical information to be reported in the journal. The patients understand that their names and initials will not be published and due efforts will be made to conceal their identity, but anonymity cannot be guaranteed.

Financial support and sponsorship

Nil.

Conflicts of interest

There are no conflicts of interest.

References

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4Couchouron T, Masson C. Early-onset progressive osteoarthritis with hereditary progressive ophtalmopathy or Stickler syndrome. Jt Bone Spine 2011;78:45-9.
5Taylor D. The Doyne lecture. Congenital cataract: The history, the nature and the practice. Eye 1998;12:9-36.